LACTONEOTETRAOSYLCERAMIDE
\lˈaktə͡ʊnˌə͡ʊttɹe͡ɪˌɒsɪlsɪɹˌama͡ɪd], \lˈaktəʊnˌəʊttɹeɪˌɒsɪlsɪɹˌamaɪd], \l_ˈa_k_t_əʊ_n_ˌəʊ_t_t_ɹ_eɪ_ˌɒ_s_ɪ_l_s_ɪ_ɹ_ˌa_m_aɪ_d]\
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Glycosphingolipids containing N-acetylglucosamine (paragloboside) or N-acetylgalactosamine (globoside). Globoside is the P antigen on erythrocytes and paragloboside is an intermediate in the biosynthesis of erythrocyte blood group ABH and P 1 glycosphingolipid antigens. The accumulation of globoside in tissue, due to a defect in hexosaminidases A and B, is the cause of Sandhoff disease.
By DataStellar Co., Ltd
Word of the day
basidiomycota
- comprises fungi bearing the spores on basidium: Gasteromycetes (puffballs); Tiliomycetes (comprising orders Ustilaginales (smuts) and Uredinales (rusts)); Hymenomycetes (mushrooms; toadstools; agarics; bracket fungi); in some classification systems considered a division of kingdom comprises fungi bearing spores on a basidium; includes Gasteromycetes (puffballs) Tiliomycetes comprising the orders Ustilaginales (smuts) and Uredinales (rusts) Hymenomycetes (mushrooms, toadstools, agarics bracket fungi).
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